Peripheral primitive neuroectodermal tumor of the upper limb: A case report and review of literature

• Author Details:   
• Sarah Afzal ^*
• Alen Thomas
• Osamah Rahman Khan

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Peripheral Primitive Neuroectodermal Tumors (pPNET) are rare malignant tumors characterized by small round cells of neuroectodermal origin. They usually occur between the age of 6-25 years, mostly in soft tissues or bones and belong to the Ewing Sarcoma Family of Tumors (ESFT). We report an unusual case of pPNET of the upper extremity in a 24-year-old male. The purpose of reporting this case is it being a rare diagnosis which demands early detection and treatment as the presence or absence of metastasis is the most significant prognostic factor.